An adamantinoma of the tibia associated with morphologic aspects of os
teofibrodysplasia is studied. The ipsilateral fibula has radiological
lesions. The first diagnosis was osteofibrodysplasia and the adamantin
oma was recognised eighteen years later. Twenty six cases of adamantin
oma associated with osteofibrodysplasia have been published in the lit
erature until 1991. The relationship between these two entities is emp
hasized. This kind of adamantinoma would have a better behaviour than
the others.