BILATERAL KERATOCONUS IN CROUZONS SYNDROME

Crouzon's syndrome is an autosomal dominant disorder characterized by premature craniosynostosis leading to multiple ocular abnormalities an d vision loss. Strabismus, optic atrophy, exposure keratitis, hypertel orism, nystagmus, and unexplained visual loss have been reported. Kera toconus has been described only once previously in a patient with othe r ocular abnormalities. This article reports bilateral keratoconus in a patient with Crouzon's syndrome without other ocular pathology. We e mphasize the importance of early recognition and therapy of this treat able cause of decreased vision in Crouzon's syndrome.