Crouzon's syndrome is an autosomal dominant disorder characterized by
premature craniosynostosis leading to multiple ocular abnormalities an
d vision loss. Strabismus, optic atrophy, exposure keratitis, hypertel
orism, nystagmus, and unexplained visual loss have been reported. Kera
toconus has been described only once previously in a patient with othe
r ocular abnormalities. This article reports bilateral keratoconus in
a patient with Crouzon's syndrome without other ocular pathology. We e
mphasize the importance of early recognition and therapy of this treat
able cause of decreased vision in Crouzon's syndrome.