Echocardiographic examination of a newborn infant showed a double outl
et right ventricle with subpulmonary ventricular septal defect. The le
ft atrium was divided by a membrane-like structure into a proximal cha
mber receiving pulmonary veins and a distal compartment containing lef
t atrial appendage. To our knowledge, this is the first report of cor
triatriatum sinistrum associated with double outlet right venticle.