L. Schmets et al., DOUBLE PORTAL AND HEPATIC VENOUS THROMBOS IS REVEALING A PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA AND REGRESSIVE WITH HEPARIN, Gastroenterologie clinique et biologique, 17(12), 1993, pp. 955-958
Budd-Chiari syndrome with or without portal thrombosis occurring durin
g paroxysmal noctural hemoglobinuria is a complication with poor progn
osis. We report the case of a 17-year-old woman with a double portal a
nd hepatic venous thrombosis revealing a paroxysmal noctural hemoglobi
nuria and regressive with heparin. Our case suggests that the early di
agnosis of the thrombosis with ultrasonography and Doppler, and rapidl
y initiated anticoagulant treatment may improve the prognosis of this
disease.