We report a rare case of multiple retroperitoneal schwannomas, initial
ly believed to be an adrenal carcinoma with metastasis. These benign t
umors were discovered in a patient presenting with vague back pain. Pr
eoperative radiographic and endocrine evaluations suggested a nonfunct
ioning adrenal tumor. The final diagnosis and its juxta-adrenal origin
were confirmed by histological and immunohistochemical studies. A rev
iew of the literature on retroperitoneal schwannoma is included.