M. Haddersalgra et al., INFANTILE CHOREA IN AN INFANT WITH SEVERE BRONCHOPULMONARY DYSPLASIA - AN EMG STUDY, Developmental Medicine and Child Neurology, 36(2), 1994, pp. 177-182
Recently a new movement disorder has been described which develops in
some preterm infants with bronchopulmonary dysplasia. The present repo
rt provides a detailed description (including polyelectromyographical
and serial cranial ultrasound findings) of this syndrome in a single i
nfant. The authors suggest that the movement disorder be called infant
ile chorea, because the movement characteristics and EMG bursting patt
ern resemble those of adult chorea. It is hypothesized that 'infantile
chorea', which is assumed to be caused by dysfunction of the striato-
thalamic circuitry, emerges at the age of two to three months post-ter
m as thalamo-corticaI connections are supposed to become functionally
active.