We report a Japanese girl with atypical lipodystrophia centrifugalis a
bdominalis infantilis. The initial lesion developed on the neck as an
area of erythema which showed centrifugal spread to the nape, submandi
bular area and upper breast and central fading to leave a residual dep
ression and purplish brown pigmentation symmetrically. A central depre
ssion on the neck, nape, submandibular area and upper breast was surro
unded by a distinctive erythematous, slightly elevated and indurated b
order. Histological examination of the erythematous border revealed in
flammatory changes in the subcutaneous fat. Although this patient was
affected in an unusual site, we concluded that she had lipodystrophia
centrifugalis abdominalis infantilis, because of the overall features
of the lesions.