M. Onerci et al., AUDIOLOGICAL AND IMPEDANCEMETRIC FINDINGS WITHIN THALASSEMIC PATIENTS, International journal of pediatric otorhinolaryngology, 28(2-3), 1994, pp. 167-172
The objective of this study is to investigate hearing losses in thalas
saemic patients. This study was conducted on 34 thalassaemic patients
of which 27 of them had thalassaemia major and the remaining 7 had tha
lassaemia intermedia. Six (11.11%) of the 54 ears with thalassaemia ma
jor were found to have normal hearing. Thirty-two ears (59.26%) had co
nductive hearing loss, 8 ears (14.81%) had mixed type of hearing loss.
Moreover, in this group, there was no ear which had pure sensorineura
l hearing loss. Of the majority of patients having thalassaemia major
and thalassaemia intermedia, an air bone gap was found even though the
re was no negative pressure in the middle ear. In these patients a hig
h degree of static compliance and normal shaped, stiff amplitude, norm
al pressure tympanograms were observed. Moreover, in most of these pat
ients acoustic reflexes were not obtained. These findings are rather i
nteresting since they show the pathological changes which may cause st
iffness in the middle ear sound transmission system.