ESTHESIONEUROBLASTOMA PRESENTING AS AN ORBITAL MASS IN A YOUNG-CHILD

A 3-year-old boy presented with uniocular proptosis and ophthalmoplegi a. Investigation revealed a mass involving the right orbit with extens ion into the left orbit and paranasal sinuses, and intracranial extens ion involving both frontal lobes. Biopsy of an enlarged cervical node and the intranasal mass revealed esthesioneuroblastoma. This tumor has been reported rarely in a child this age, and only 12 case reports do cument patients under 10 years of age. The presentation as an orbital mass is previously unreported and must now be considered in the differ ential diagnosis of proptosis in childhood. The usual clinical, radiol ogical, and pathological features of olfactory esthesioneuroblastoma a re reviewed. (C) 1994 Wiley-Liss, Inc.