We report 2 cases of dermatitis herpetiformis (DH) with lymphoma: a no
n-Hodgkin's malignant histiocytic lymphoma and a rare phenotype of Hod
gkin's disease. With these 2 cases, 32 cases of DH complicated by lymp
homa have now been documented. Reviewing the literature we show that t
he majority of,lymphomas (78.1%) arises from the gastro-intestinal tra
ct and that almost all cases of DH with lymphoma are associated with c
oeliac disease. The possible preventive role of a gluten-free diet is
discussed.