TYPE-I GLYCOGENOSIS WITH RENAL TUBULAR DYSFUNCTION - (PRESENTATION OF2 CASES)

Authors
YUCE A COSKUN T KOCAK N OZSOYLU S OZALP I GOGUS S
Citation
A. Yuce et al., TYPE-I GLYCOGENOSIS WITH RENAL TUBULAR DYSFUNCTION - (PRESENTATION OF2 CASES), Turkish Journal of Pediatrics, 35(3), 1993, pp. 201-204
Citations number
NO
Categorie Soggetti
Pediatrics
Journal title
Turkish Journal of Pediatrics → ACNP
ISSN journal
00414301
Volume
35
Issue
3
Year of publication
1993
Pages
201 - 204
Database
ISI
SICI code
0041-4301(1993)35:3<201:TGWRTD>2.0.ZU;2-E
Abstract
Two patients with hepatic glycogenosis associated with Fanconi syndrom e are presented. Both patients were treated with a neutral phosphorus solution, an oral alkaline solution, cholecalciferol and uncooked corn starch. The proximal renal tubular functions were corrected in the pat ient who used cornstarch properly, which may indicate a causal relatio nship between Fanconi syndrome and glycogenosis.