Moyamoya disease is one of the cerebrovascular disorders and is charac
terized by bilateral stenosis or occlusion of the distal internal caro
tid arteries and their main branches. Repeated ischemic episodes in ch
ildren and intracranial hemorrhage in adults with moyamoya disease is
usually noted. In this report, we describe two children with moyamoya
disease who presented with alternating hemiplegia. The final diagnosis
was made by cerebral angiography and cranial computed tomography in t
hese patients. Other neurological and radiological features of the pat
ients were described.