E. Fernell et al., INFANTILE HYDROCEPHALUS EPIDEMIOLOGY - AN INDICATOR OF ENHANCED SURVIVAL, Archives of Disease in Childhood, 70(2), 1994, pp. 60000123-60000128
The epidemiology of infantile hydrocephalus in the birth years 1973-90
was investigated in west Sweden. The study revealed a significant inc
rease in prevalence from 1973-8 and 1979-82 considered due to the enha
nced survival of very and extremely preterm infants. The increase did
not continue from 1983-90. This could indicate an improved outcome in
preterm survivors as the neonatal survival rate continued to increase.
The striking predominance of a perinatal/neonatal aetiology in very p
reterm hydrocephalic infants could be confirmed: 89% born from 1983-90
had suffered a confirmed postpartum intraventricular haemorrhage. In
infants born at term, prenatal origins, mainly maldevelopments, domina
ted. The outcome in very preterm surviving infants with infantile hydr
ocephalus was poor: 73% had cerebral palsy, 52% epilepsy, 22% severe v
isual disability, and 55% were mentally retarded. Despite the increase
d survival resulting in a majority of healthy infants, there is an acc
umulating cohort of hydrocephalic children.