CEREBRAL RHABDOMYOSARCOMA WITH RHABDOID TUMOR-LIKE FEATURES

The present paper describes a case of cerebral neoplasm presenting his tological-immunohistochemical characteristics of malignant rhabdoid tu mor (MRT) and ultrastructural features of both MRT and rhabdomyosarcom a (R). MRT was first described as an aggressive neoplasm of unknown hi stogenesis of the kidney, then many other sites of onset were reported , including the central nervous system. However, it has been shown tha t other tumors of known histogenesis can mimick histologic and ultrast ructural features of MRT. On the basis of our findings we agree with a uthors who support the notion that extrarenal MRT has often a differen t histogenesis from MRT of kidney, and it probably is a 'phenotypic' e ntity rather than a distinct pathologic entity.