A 41/2-year-old girl with incontinentia pigmenti developed acute-onset
hemiparesis. Magnetic resonance angiography revealed occlusion of the
left middle cerebral artery. Many neurocutaneous syndromes have been
linked to ischemic stroke syndromes. Incontinentia pigmenti has not be
en associated with stroke syndromes in the past; however, this report
illustrates that the patient and her mother, who also has incontinenti
a pigmenti, may have had similar ischemic stroke events.