MENINGEAL MENINGIOMATOSIS IN A CHILD - CASE-REPORT

We report a child with multifocal meningeal lesions demonstrating mixe d meningiomatous histologic features. This lesion appears to have evol ved over seven years, starting with a brief episode of garbled speech, nausea, and headache at 4.5 years of age. The child was then asymptom atic until 9 when she presented with bilateral leg weakness, in additi on to her prior presenting symptoms and communicating hydrocephalus. M eningeal biopsies of two lesions were performed 18 months later. Immun ohistochemistry and electron microscopy were needed to substantiate th e histologic diagnosis. Radiation therapy to the craniospinal axis and corticosteroids were of some benefit. but more aggressive therapeutic modalities became necessary. The nosology of this lesion is discussed .