The case of a male child with a benign neurogenic laryngeal tumour cau
sed by von Recklinghausen's disease is presented. At the age of eight
years, tracheostomy was necessary. The tumour, deforming the right hal
f of the larynx and extending into the right half of the neck, was rem
oved three years later. Following this procedure, decannulation was po
ssible, and the patient has been free of laryngological complaints for
six years. Attention is drawn to the fact that autosomal dominantly i
nherited neurofibromatosis is a generalized benign tumour with a speci
al form. If it involves any vital structure or forms a functional obst
acle, meticulous surgical removal is necessary, and this provides good
prospects over a long period.