ANESTHESIA AND THE STURGE-WEBER SYNDROME

We report a series of 13 patients with Sturge-Weber syndrome anaesthet ised on 17 occasions. Anaesthesia management varied depending on the c linical manifestations which ranged from localized, superficial skin l esions to extensive systemic involvement. These patients tolerate anae sthesia well but anaesthetic management includes evaluation for associ ated anomalies. Difficulty with intubation may occur due to angiomas o f the mouth and upper airway. Anaesthesia should be planned to avoid t rauma to the haemangiomata and increases in intraocular and intracrani al pressure.