RENAL ANGIOMYOLIPOMA AND PULMONARY LYMPHA NGIOMYOMATOSIS - A NON-HAZARDOUS ASSOCIATION

Angiomyolipoma is a rare tumor, frequently associated with tuberous sc lerosis, but not observed in its isolated form. Usually, patients with tuberous sclerosis presented with pathognomonic cutaneous and central nervous system lesions. But the thesis of 'formes frustes'' without t ypical stigmata was suggested. A case of bilateral and multifocal angi omyolipoma in a young woman without evidence of phacomatosis is report ed. The association with a pulmonary lymphangiomatosis make us suspect ed ''a forme fruste '' of tuberous sclerosis.