PRIMARY RHABDOID TUMOR OF THE SKIN IN A 14-MONTH-OLD CHILD

We report on a primary cutaneous rhabdoid tumour in a 14-month-old chi ld, to the best of our knowledge, the second case in the literature. T he tumour showed a multipolypoid gross appearance and classical histol ogical features. The neoplastic cells were positive for keratin and vi mentin and most were positive for proliferating cell nuclear antigen. The ultrastructural examination revealed typical intracytoplasmic aggr egates of intermediate filaments. The tumour showed a very aggressive course, and the child died 5 months after the diagnosis of cerebral me tastasis.