A VARIANT OF CENTRAL AREOLAR CHOROIDAL DYSTROPHY

This article describes the variable ophthalmoscopic features of a macu lar disorder in five generations of one family. This disease shares si milarities with central areolar choroidal dystrophy and other progress ive dominant macular dystrophies but demonstrates significant differen ces that required further consideration. The milder affected individua ls had confluent hyperfluorescence around the macular area while the m ore severe lesions consisted of marked chorioretinal atrophy of the ma cula. The visual fields revealed a central scotoma. The disorder was t ransmitted as an autosomal dominant trait.