JAFFE-CAMPANACCI SYNDROME - CASE-REPORT

Jaffe-Campanacci syndrome is a rare entity caracterized by disseminate d non ossifying fibromas in association with extraskeletal congenital anomalies: cutaneous, genital, ocular and cardiovascular. Mental retar dation is also frequently observed. Pathological fractures are the usu al merle of revelation. We report one case original because of causal discovery during orthodontic check-up and because of extraskeletal ano malies not previously described. In fact the true incidence of this sy ndrome is probably underestimated because of unrecognized features.