LEFT OVARIAN-CYST AND RIGHT STREAK OVARY IN A NEONATE WITH A NORMAL KARYOTYPE - REPORT OF A CASE OF NEONATAL SLOTNICK-GOLDFARB SYNDROME OR RECESSIVE GONADAL-DYSGENESIS

A female neonate with a streak ovary on one side and huge ovarian cyst on the other side is presented. Her karyotype teas 46,XX. Adnexectomy tons mandatory, leaving the patient with a single streak gonad. Wheth er this infant has the recessive form of gonadal dysgenesis with one o vary, streak or hypoplastic, replaced by a cyst or the Slotnick-Goldfa rb syndrome is impossible to elucidate at present. The potential impli cations of a streak gonad, either related to gonadal dysgenesis or as a possible source of neoplasia, are reviewed. Current approaches to an ovarian cyst and streak ovary in the neonatal period are discussed.