LEFT OVARIAN-CYST AND RIGHT STREAK OVARY IN A NEONATE WITH A NORMAL KARYOTYPE - REPORT OF A CASE OF NEONATAL SLOTNICK-GOLDFARB SYNDROME OR RECESSIVE GONADAL-DYSGENESIS
E. Freud et al., LEFT OVARIAN-CYST AND RIGHT STREAK OVARY IN A NEONATE WITH A NORMAL KARYOTYPE - REPORT OF A CASE OF NEONATAL SLOTNICK-GOLDFARB SYNDROME OR RECESSIVE GONADAL-DYSGENESIS, Journal of reproductive medicine, 39(4), 1994, pp. 318-320
A female neonate with a streak ovary on one side and huge ovarian cyst
on the other side is presented. Her karyotype teas 46,XX. Adnexectomy
tons mandatory, leaving the patient with a single streak gonad. Wheth
er this infant has the recessive form of gonadal dysgenesis with one o
vary, streak or hypoplastic, replaced by a cyst or the Slotnick-Goldfa
rb syndrome is impossible to elucidate at present. The potential impli
cations of a streak gonad, either related to gonadal dysgenesis or as
a possible source of neoplasia, are reviewed. Current approaches to an
ovarian cyst and streak ovary in the neonatal period are discussed.