PROTEUS-SYNDROME - CLINICAL-FEATURES AND DIFFERENTIAL-DIAGNOSIS

A case with various skeletal abnormalities, soft tissue masses and ski n lesions diagnosed as Proteus syndrome is reported. Proteus syndrome is included in the differential diagnosis of many disorders, because o f the polymorphous nature of its clinical manifestations. It is a rare disorder and leads to functional disabilities as well as cosmetic and psychological problems. Early diagnosis and careful follow-up with ap propriate surgical interventions is important in preventing long-term complications.