OBJECTIVE AND IMPORTANCE: Cases of intraorbital arteriovenous malforma
tions are rare, and their management presents a challenge for multidis
ciplinary teams.CLINICAL PRESENTATION: A 39-year-old woman developed a
pulsating exophthalmos, visual loss, and ocular pain within 1 month,
revealing the presence of intraorbital arteriovenous malformations. Sh
e underwent only surgical treatment. INTERVENTION: A fronto-orbital ap
proach with removal of the orbital rim was performed. A CO, laser faci
litated all the surgical steps. CONCLUSION: Full recovery of vision an
d correction of the proptosis have been achieved, and postoperative ma
gnetic resonance imaging and angiography confirmed the total removal o
f the malformations. The literature is reviewed regarding the manageme
nt of such lesions. Surgery remains the treatment of choice. The role
of embolization is discussed.