We describe a rare case of cervical canal stenosis at the level of the
atlas, presenting with cervical myelopathy as an initial symptom. A 5
5-year-old man was admitted to our hospital with a 4-month history of
gait disturbance and clumsiness in both hands. He had no history of tr
auma, and showed left-sided hemihyperesthesia and mild quadriplegia wi
th exaggerated deep tendon reflexes. Plain cervical tomography reveale
d marked spinal canal stenosis, with the diameter of 8.0 mm at the lev
el of the atlas. Magnetic resonance imaging demonstrated severe compre
ssion of the spinal cord at the atlas with an extensive high intensity
area indicating edema on T2-weighted images. The patient showed an ex
cellent recovery after laminectomy of the atlas combined with decompre
ssion of the lower posterior fossa of the foramen magnum and dural pla
sty.