Leiomyosarcomas of the rectum are uncommon neoplasms accounting for fe
wer than 1% of all malignancies of the colon and rectum. Approximately
215 cases have been described in the literature. Distinction from lei
omyoma is often difficult, but regarding dignity is important. The cas
e reported is that of a 68-year-old man in whom a 2.2-cm rectal mass c
overed by mucosa was diagnosed by rectoscopy and endorectal ultrasound
. After treatment by wide local excision the histological specimen rev
ealed a low-grade, highly differentiated leiomyosarcoma. Due to the la
ck of a large series of this disease, there is disagreement over the t
herapeutic strategy. At the moment a selective treatment approach seem
s to be the most frequently advocated. Large tumors and those extendin
g beyond the rectal wall are treated by radical surgical resection. Le
imyosarcomas less than 2.5 cm in size and confined to the bowel wall c
an be treated by wide local excision. Endosonography can provide exact
assessment of tumor size and expansion and is of great value in selec
ting the appropriate treatment.