COEXISTING LYMPHANGIOLEIOMYOMATOSIS AND BILATERAL ANGIOMYOLIPOMAS IN A PATIENT WITH TUBEROUS SCLEROSIS

Authors
UZZO RG LIBBY DM VAUGHAN ED LEVEY SH
Citation
Rg. Uzzo et al., COEXISTING LYMPHANGIOLEIOMYOMATOSIS AND BILATERAL ANGIOMYOLIPOMAS IN A PATIENT WITH TUBEROUS SCLEROSIS, The Journal of urology, 151(6), 1994, pp. 1612-1615
Citations number
38
Categorie Soggetti
Urology & Nephrology
Journal title
The Journal of urology → ACNP
ISSN journal
00225347
Volume
151
Issue
6
Year of publication
1994
Pages
1612 - 1615
Database
ISI
SICI code
0022-5347(1994)151:6<1612:CLABAI>2.0.ZU;2-1
Abstract
A patient with tuberous sclerosis and known bilateral angiomyolipomas presented with a complete pneumothorax prior to scheduled renal surger y. Evaluation revealed the presence of pulmonary lymphangioleiomyoma, an unusual entity known to coexist with tuberous sclerosis. Pulmonary decortication and conservative renal surgery resulted in a satisfactor y long-term result.