UNCOMBABLE HAIR SYNDROME - PILI-TRIANGULI-ET-CANALICULI WITH CONCOMITANT TRICHOPTILOSIS ON SCANNING ELECTRON-MICROSCOPY

The uncombable hair syndrome (UHS) is a rare disorder with usual onset in infancy. It is characterized clinically by dry, frizzy, spangled a nd unruly hair. Evaluation with the scanning electron microscopy (SEM) characteristically shows longitudinal grooving of the hair shafts. We present a case in which trichoptilosis was also noted on SEM. This fi nding has not been previously reported in this condition. A review of reported features of UHS is also included.