Four patients presenting with high grade unilateral vesicoureteral ref
lux were discovered at surgery to have an unsuspected duplex system wi
th a ureterocele associated with the upper pole of the refluxing kidne
y. No preoperative radiographic study was diagnostic for duplication o
r ureterocele but when studies were reviewed retrospectively subtle ev
idence suggesting this possibility could be identified in a few cases.
This rare situation should be considered whenever massive unilateral
vesicoureteral reflux is encountered.