A rare case of pseudomyxoma peritonei whose primary site was presumed
to be the lung is reported. A 76-year-old woman was admitted to Hospit
al presenting with progressive abdominal distention. She had been admi
tted twice, 2 and 1 year previously for the evaluation of high plasma
carcinoembryonic antigen (CEA) level, of 11.6 ng/ml. Chest computed to
mography (CT) scan and chest X-ray film on the third admission reveale
d a nodular lesion in the left lower lung field, and transbronchial lu
ng biopsy (TBLB) revealed mucus-producing tall columnar epithelial car
cinoma. Paracentesis revealed gelatinous ascitic fluid. At laparotomy,
appendix and ovary were normal, and there were many small cystic tumo
rs on the peritoneal surface and omentum. The patient died 2 years lat
er, after repeated episodes of dynamic ileus. The lung and abdominal t
umors gradually increased in size during the 2-year period, but she de
veloped no respiratory symptoms. Based on both the clinical and pathop
hysiological findings, the final diagnosis made was pseudomyxoma perit
onei whose origin was a lung adenocarcinoma.