Cardiac angiosarcoma is a rare tumour with very poor prognosis especia
lly in patients with metastatic disease. We present the case of a 43 y
ear old patient with angiosarcoma revealed by open lung biopsy for mul
tiple pulmonary metastases. Cardiac symptoms were limited to a moderat
e pericarditis and no echocardiographic sign of heart tumour was obser
ved. The clinical outcome was rapidly fatal despite chemotherapy. The
cardiac primary tumour was diagnosed at autopsy. We emphasize the diff
iculties of diagnosing cardiac angiosarcoma and confirm the limited va
lue of echocardiography for this diagnosis.