3 CASES OF HEREDITARY DEAFNESS POSSIBLY DUE TO BRAIN-STEM LESIONS

In this report, 3 cases of deafness resulting from possibly autosomal recessive disorders affecting the brainstem with no other pathologies or health problems are presented. The common characteristics of these patients are the presence of an unknown functional lesion in the brain stem as documented by the auditory brainstem response testing. Radiolo gical, behavioral and physiological test results are presented for the first time to support a hereditary deafness symptom that might arise from interfamily marriages.