ELECTROCARDIOGRAPHIC FINDINGS IN RETT-SYNDROME - AN EXPLANATION FOR SUDDEN-DEATH

Authors
SEKUL EA MOAK JP SCHULTZ RJ GLAZE DG DUNN JK PERCY AK
Citation
Ea. Sekul et al., ELECTROCARDIOGRAPHIC FINDINGS IN RETT-SYNDROME - AN EXPLANATION FOR SUDDEN-DEATH, The Journal of pediatrics, 125(1), 1994, pp. 80-82
Citations number
9
Categorie Soggetti
Pediatrics
Journal title
The Journal of pediatrics → ACNP
ISSN journal
00223476
Volume
125
Issue
1
Year of publication
1994
Pages
80 - 82
Database
ISI
SICI code
0022-3476(1994)125:1<80:EFIR-A>2.0.ZU;2-Q
Abstract
Girls with Rett syndrome had significantly longer corrected QT interva ls (p <0.001) and more T-wave abnormalities (p <0.001) than were found in age-matched healthy girls. With advancing stages of the syndrome, the proportion of corrected QT interval prolongations and T-wave chang es increased. The findings suggest a possible cardiac basis for sudden , unexpected death in Rett syndrome.