Fifty-three patients with neurogenic orbital tumors were diagnosed and
treated at our university hospital during the past three decades. The
re were 16 patients with juvenile pilocytic astrocytomas, 21 patients
with meningiomas and 16 with peripheral nerve tumors. Of the 16 periph
eral nerve tumor patients, 8 had schwannoma, 4 had neurofibroma, 2 had
malignant schwannoma, one had paraganglioma and one had amputation ne
uroma. Optic nerve tumors were treated via a transfrontal craniotomy i
f there was no chiasmal involvement. Cases with chiasmal involvement,
incomplete resections and recurrences were treated with radiotherapy (
5000 cGy). Far advanced cases with progressive proptosis and ocular da
mage underwent exenteration. Peripheral nerve tumors were treated by l
ocal resection. Exenteration was applied when there was an advanced or
malignant lesion. Four of the 16 glioma patients and 5 of the 21 meni
ngioma patients died during follow-up. The prognosis for peripheral ne
rve tumors was generally good, except for malignant schwannomas. Two p
atients with this malignant tumor died within 2 years after surgery.