It is rare for solitary basal cell cancer not to be associated with th
e naevoid basal cell carcinoma syndrome (NBCCS), xeroderma pigmentosum
, an organoid nevus or X-ray therapy in children (to date 86 cases hav
e been documented in the literature. Aetiologically, the tumours might
be a forme fruste of the NBCCS or they might follow a somatic point m
utation of keratinocytes. Up to now, data on the repair mechanism foll
owing UV-induced DNA damage are not available in these patients. We re
port on a 10-year-old boy with a solitary nodular basal cell cancer in
the right malar region. Neither the patient's history nor the clinica
l findings suggested a genetic disposition to development of the tumou
r.