SUCCESSFUL REPAIR OF THE RIGHT ATRIAL ISOMERISM, DOUBLE-OUTLET RIGHT VENTRICLE, COMMON ATRIOVENTRICULAR-CANAL, PULMONARY STENOSIS, AND TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION

A 6-year-old boy was successfully operated on for double outlet ventri cle, common atrioventricular canal with severe valvular regurgitation, right atrial isomerism, L-loop ventricles, total anomalous pulmonary venous connection, and pulmonary stenosis with hypoplastic left pulmon ary artery. The interventricular rerouting from the left ventricle to the ascending aorta was performed with a spiral patch, the interatrial switching was performed by a Mustard patch, the common atrioventricul ar orifice was partitioned and valve repair was performed, and an 18-m m valved conduit was inserted between the right ventricle and the pulm onary artery. Although the patient had a small residual ventricular se ptal defect and pulmonary stenosis, the patient is alive and well.