KERATOCONUS IN MULVIHILL-SMITH SYNDROME

Background The Mulvihill-Smith syndrome consists of a large number of stigmata. A few of them are also seen in the LEOPARD syndrome. In both syndromes keratoconus has not yet been reported. Patient We present a twenty-year-old male patient suffering from keratoconus in connection with a Mulvihill-Smith syndrome. A keratoplasty a chaud was done afte r perforation of the corneal ulcer. Conclusion As a major complication corneal graft rejection is known after keratoplasty a chaud. However, in our patient immunological graft failure may be prevented by the T- cell defect.