Trigonocephaly mostly occurs in isolated synostosis of the metopic sut
ure, but 10-20% of patients are affected by complex syndromes, and in
2-5% the condition is familial. Intracranial hypertension has been obs
erved in a minority of cases, but is never severe. Surgery is performe
d mainly for cosmetic reasons, following the standard principles of cr
aniofacial surgery. Complications are rare and satisfactory cosmetic r
esults are generally obtained. There is little likelihood of recurrent
deformity.