Ka. Taubert et al., 7-YEAR NATIONAL SURVEY OF KAWASAKI-DISEASE AND ACUTE RHEUMATIC-FEVER, The Pediatric infectious disease journal, 13(8), 1994, pp. 704-708
To assess the frequency of hospital encoded diagnoses of acute rheumat
ic fever (ARF) and Kawasaki disease (KD), the two leading causes of ac
quired heart disease in children in the United States, we performed a
survey of the medical record departments of United States children's h
ospitals and of general hospitals that have at least 400 beds and a pe
diatric ward. With a simple questionnaire, data were gathered for the
years 1984 through 1990 by ICD.9CM codes, with a 58% response rate. Ab
out 8000 diagnoses of KD and 6000 diagnoses of ARF were encoded during
the study period. Encoded diagnoses of both KD and ARF showed yearly
fluctuations in the earlier years (1984 through 1987). For KD there wa
s a general trend toward increasing numbers after 1986. These data are
consistent with increased physician awareness and diagnosis of KD. Fo
r ARF a gradual decline was observed between 1986 and 1990. About 80%
of ARF diagnoses were reported from general hospitals. The much smalle
r pool of encoded diagnoses of ARF at the children's hospitals showed
a 56% increase from 1985 to 1986. These data suggest that the highly p
ublicized increase in cases of acute rheumatic fever in the United Sta
tes during the mid-1980s may reflect focal rather than nationwide incr
eased activity and that nationally the number of diagnoses of ARF actu
ally may have continued to decline gradually from 1984 through 1990.