Granulomatous angiitis is a rare, treatable central nervous system vas
culitis. Prompt diagnosis may be thwarted by protean presenting sympto
ms, an indolent clinical course, and atypical neurological findings. T
he authors describe a case of indolent granulomatous angiitis in which
the patient presented with cerebellar signs and tissue changes sugges
tive of an atypical cerebellar infarction. After several years of remi
ssions and relapses, repeat evaluation and biopsy disclosed granulomat
ous angiitis both in remote infarctions and in new cortical lesions. T
he clinical course and neuroradiological and pathological findings are
compared with previous reports of fulminant and indolent granulomatou
s angiitis.