N. Cailleux et al., PSEUDOXANTHOMA ELASTICUM - A RARE CAUSE O F LOWER-LIMB ARTERITIS IN YOUNG-ADULTS, Journal des maladies vasculaires, 22(1), 1997, pp. 51-55
Pseudoxanthoma elasticum (PXE) is a rare inherited connective tissue d
isorder which is characterized by elastic tissue degeneration involvin
g the skin, eyes and arteries. We describe the case of a hypercholeste
rolemic 25 year-old woman with typical genetic dominant form of PXE re
vealed by distal limb artery involvement after a pregnancy. In young a
dults with arterial disease, a non atheromatous cause should always be
sought for, even if risk factors for atherosclerosis are present (J M
al Vasc 1997; 22 : pages 51-55).