GIANT CONGENITAL JUVENILE XANTHOGRANULOMA

Congenital giant juvenile xanthogranuloma is an uncommon lesion that a pparently has benign biologic behavior in most reported patients. In o ne of our three patients it was necessary to perform histochemical rea ctions with CD 1 (-), MAC 387, and electron microscopy to rule out Lan gerhans cell histiocytosis. The other patients had a typical histologi c picture, with foamy histiocytes and Touton cells in association with lymphocytes and eosinophils. Comments about treatment are also made.