Angioid streaks associated with pseudoxanthoma elasticum (Gronblad-Str
andberg syndrome) usually are described in young adults. We report the
case of a ten-year-old boy with angioid streaks and peau d'orange dis
coloration of both ocular fundi associated with pseudoxanthoma elastic
um. This represents, to the best of our knowledge, the youngest patien
t with this association reported in the ophthalmic literature.