SELECTIVE IGA DEFICIENCY PRESENTING WITH HYPERSPLENISM

A young patient presenting with splenomegaly and hypersplenism was ina dvertently found to have selective IgA deficiency. There were no sympt oms of immunodeficiency and the patient responded well to splenectomy, with return of blood counts to normal without adverse effects. No oth er cause for the hypersplenism was found. We postulate selective IgA d eficiency as a cause of splenomegaly and hypersplenism.