Aortoesophageal fistula (AEF) is a rare but frequently lethal cause of
upper gastrointestinal bleeding. This is a report of the authors' exp
erience with four cases-two from congenital and two from acquired caus
es. A review of the pediatric cases reported in the literature is incl
uded. The mortality from AEF is high, and can be decreased in two ways
. AEF can be prevented by avoiding prolonged nasogastric intubation in
patients with known vascular rings, and by promptly removing esophage
al foreign bodies and promptly treating periesophageal abscesses. Once
an AEF occurs, it presents with typical large-herald upper gastrointe
stinal bleeding of bright red blood, and cardiovascular collapse. Reco
gnition of this pattern, with vigorous resuscitation and aggressive su
rgical management, will improve the survival rate. Copyright (C) 1994
by W.B. Saunders Company