DYSPLASIA EPIPHYSEALIS HEMIMELICA WITH AT YPICAL INVOLVEMENT OF THE BREAST

A 2 8/12 year old boy presented with osteochondromata of the sternum, left clavicle, proximal epiphysis of the left humerus, and of the left carpalia as features of dysplasia epiphysealis hemimelica (Trevor-syn drome). The clavicle showed a lateral osteolysis. This is the first de scription of the involvement of sternum and clavicle. In cases with se emingly rapid onset the differential diagnosis of Trevor-syndrome incl udes malignancies. Modern imaging methods are not superior to conventi onal radiography which can establish the correct diagnosis especially when carpalia or tarsalia are involved.