ARTERIAL FIBRODYSPLASIA CAUSING OCCLUSIVE VASCULAR-DISEASE SIMULATINGPRIMARY VASCULITIS

We report a case of arterial fibrodysplasia causing vascular disease w ith ulceronecrotic lesions in lower extremities. The arteriography sho wed a beaded pattern in both arteries and veins; laboratory test findi ngs were within normal value ranges; the biopsy reported medial hyperp lasia involving the arterial and venous walls. Arterial fibrodysplasia should be considered as a differential diagnosis in patients complain ing of recurrent occlusive vascular episodes without systemic manifest ations, normal laboratory test results, and radiological patterns sugg estive of fibrodysplasia. This is the first report of medial hyperplas ia in digital arteries and venous wall involvement.