The authors report a case of leptomeningeal spinal metastasis of chias
matic juvenile pilocytic astrocytoma. A 7-year-old boy underwent surge
ry and radiation therapy for a chiasmatic pilocytic astrocytoma. Three
years later he experienced a syndrome of medullary compression. A lum
bosacral intradural extra-axial tumor was discovered and subtotally ex
cised. Pathologic examination revealed a metastasis of the chiasmatic
tumor without any evidence of malignant transformation. Only five case
s of leptomeningeal spinal dissemination of pilocytic astrocytoma have
been previously reported. The authors review and discuss the clinical
and pathologic features of these cases.