LHERMITTE-DUCLOS DISEASE - A CASE-REPORT

We report one case of histologically proved Lhermitte-Duclos disease. Suspected on the basis of CT and angiography, the pre-operative diagno sis has been confirmed by the characteristic features of the lesion on MRI: a unilateral posterior fossa mass, hyperintense on proton densit y and T2-weighted images, hypointense on T1-weighted images, non enhan cing after Gd administration. The gyral pattern was preserved, but a s pecific thickening of cerebellar folia was demonstrated. Despite a goo d post-operative short term prognosis, recurrence may occur. With a be tter depiction of lesion limits, MRI could improve the surgical approa ch and reduce the risk of subtotal excision.